Page 60 - MDA MIDEC 2024 Programme Book

ORAL PRESENTATION ABSTRACTS

P018 Name of Presenter: Nur ‘Afirah Binti Maluin, Hospital Tuanku Jaafar Seremban
Title of Presentation: Parry-Romberg Syndrome with Poliosis Circumscripta: A Rare Case
Report

Abstract
Afirah M 1,*, Sutina K 1, Low LF 1, Mohamad Ropi M 1
1 Oral and Maxillofacial Surgery Department, Hospital Tuanku Jaafar Seremban

Background: Parry-Romberg Syndrome (PRS) is a rare progressive degenerative disorder manifests as
hemifacial atrophy involving the skin, subcutaneous, muscle, and bone. It may or may not be associated
with neurological dysfunction, ocular changes, and dental anomalies. The presentation of this disease rarely
affects the extremities. The disease is mainly idiopathic, but often related to trauma, infections, genetic
factors or autoimmunity. Atrophy may start during the first decade of life, then slowly progressive over
the years. The disease stabilization may achieve during adulthood at 20 years of life. Although multiple
cases discovered worldwide, none have encountered the cure of this disease. Regular monitoring and
symptomatic non-invasive therapy may be provided until the disease progression ceases at certain age.
During this point, reconstructive surgery may be recommended to correct the asymmetrical of the face.
Case Report: This paper reporting a case of 10-years old Malay boy who encountered in the department
with hypopigmentation and hemimandibular atrophy on left side of the face. The characteristics match the
classical features of Parry-Romberg Syndrome, with history of trauma during early childhood.
Conclusion: Although PRS is commonly presented during childhood, the progression of this disease
typically distressing and challenging to suppress until stabilization age achieve.

Key words: Parry-Romberg Syndrome, hemifacial atrophy, hypopigmentation

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